Fukumitsu Kansai, Fujishima Kazuto, Yoshimura Azumi, Wu You Kure, Heuser John, Kengaku Mineko
Institute for Integrated Cell-Material Sciences (WPI-iCeMS) and Graduate School of Biostudies, Kyoto University, Kyoto 606-8501, Japan.
Institute for Integrated Cell-Material Sciences (WPI-iCeMS) and.
J Neurosci. 2015 Apr 8;35(14):5707-23. doi: 10.1523/JNEUROSCI.4115-14.2015.
The distribution of mitochondria within mature, differentiated neurons is clearly adapted to their regional physiological needs and can be perturbed under various pathological conditions, but the function of mitochondria in developing neurons has been less well studied. We have studied mitochondrial distribution within developing mouse cerebellar Purkinje cells and have found that active delivery of mitochondria into their dendrites is a prerequisite for proper dendritic outgrowth. Even when mitochondria in the Purkinje cell bodies are functioning normally, interrupting the transport of mitochondria into their dendrites severely disturbs dendritic growth. Additionally, we find that the growth of atrophic dendrites lacking mitochondria can be rescued by activating ATP-phosphocreatine exchange mediated by creatine kinase (CK). Conversely, inhibiting cytosolic CKs decreases dendritic ATP levels and also disrupts dendrite development. Mechanistically, this energy depletion appears to perturb normal actin dynamics and enhance the aggregation of cofilin within growing dendrites, reminiscent of what occurs in neurons overexpressing the dephosphorylated form of cofilin. These results suggest that local ATP synthesis by dendritic mitochondria and ATP-phosphocreatine exchange act synergistically to sustain the cytoskeletal dynamics necessary for dendritic development.
线粒体在成熟、分化的神经元中的分布显然是为了适应其局部生理需求,并且在各种病理条件下可能受到干扰,但线粒体在发育中的神经元中的功能研究较少。我们研究了发育中的小鼠小脑浦肯野细胞内的线粒体分布,发现线粒体向其树突的主动运输是树突正常生长的先决条件。即使浦肯野细胞体中的线粒体功能正常,中断线粒体向其树突的运输也会严重干扰树突生长。此外,我们发现,通过激活由肌酸激酶(CK)介导的ATP-磷酸肌酸交换,可以挽救缺乏线粒体的萎缩树突的生长。相反,抑制胞质CK会降低树突ATP水平,并破坏树突发育。从机制上讲,这种能量消耗似乎会扰乱正常的肌动蛋白动力学,并增强生长中的树突内丝切蛋白的聚集,这与过表达去磷酸化形式丝切蛋白的神经元中发生的情况相似。这些结果表明,树突线粒体的局部ATP合成和ATP-磷酸肌酸交换协同作用,以维持树突发育所需的细胞骨架动力学。