Fain J S, Lewin K J
Department of Pathology, UCLA Medical Center 90024-1732.
Arch Pathol Lab Med. 1989 Dec;113(12):1383-6.
A case of pronounced cystic dilatation of the intrahepatic bile ducts with biliary atresia is presented. Intrahepatic biliary cysts have been described in biliary atresia, although, as far as we are aware, none as extensive as in this case. The cysts represent end-stage obstruction with irreversible liver injury; thus, drainage of these cysts does not alleviate the condition. The differential diagnosis includes Caroli's disease, congenital hepatic fibrosis, and polycystic liver disease.
本文报告一例肝内胆管显著囊性扩张合并胆道闭锁的病例。肝内胆管囊肿在胆道闭锁中已有报道，尽管据我们所知，尚无如此广泛的病例。这些囊肿代表了终末期梗阻伴不可逆性肝损伤；因此，引流这些囊肿并不能缓解病情。鉴别诊断包括卡罗里病、先天性肝纤维化和多囊肝疾病。
