Hammarstedt Jon E, Redmond John M, Gupta Asheesh, Domb Benjamin G
1 University of Illinois at Chicago, Chicago, Illinois - USA.
Hip Int. 2015 May-Jun;25(3):286-91. doi: 10.5301/hipint.5000228. Epub 2015 Apr 23.
Ehlers-Danlos syndrome (EDS) is a genetic disorder that affects the structural integrity of collagen within the body. This presents clinically as a connective tissue disorder with increased elasticity of joints, muscles, and ligaments. Multiple joints are affected by hypermobility and joint injury is common in these patients. It is estimated that EDS occurs once in every 5,000 births worldwide.
This article focuses on reconstruction of the ligamentum teres (LT) of the hip using a tibialis anterior allograft to treat severe instability and pain in a 43 year-old female with EDS. The LT reconstruction was accompanied by labral repair and capsular plication. The patient was assessed pre- and postoperatively using modified Harris Hip Score (mHHS), Hip Outcome Score Activities of Daily Living (HOS-ADLS), Hip Outcome Score Sports Specific Subscale (HOS-SSS), Non Arthritic Hip Score (NAHS), Visual Analog Scale (VAS), and satisfaction. One year following surgery the patient has reported positive outcomes in terms of pain and instability.
Ligament reconstruction has been reported in patients with Ehlers-Danlos syndrome for shoulders and knees with positive results and restoration of stability. Currently there is a paucity of literature regarding patients with EDS undergoing hip procedures. In addition, reconstruction of the ligamentum teres for hip instability and pain has rarely been reported in a normal patient cohort.
This is the first study to report ligamentum teres reconstruction of the hip in a patient with Ehlers-Danlos syndrome and hip instability. The patient demonstrated satisfactory results 1 year from surgery.
埃勒斯-当洛综合征(EDS)是一种遗传性疾病,会影响体内胶原蛋白的结构完整性。临床上表现为一种结缔组织疾病,关节、肌肉和韧带的弹性增加。多个关节会出现活动过度,这些患者中关节损伤很常见。据估计,全球每5000例出生中就有1例发生EDS。
本文重点介绍了一名43岁患有EDS的女性,采用同种异体胫骨前肌移植重建髋关节圆韧带(LT),以治疗严重的不稳定和疼痛。LT重建同时进行了髋臼唇修复和关节囊折叠术。使用改良Harris髋关节评分(mHHS)、髋关节功能评分日常生活活动量表(HOS-ADLS)、髋关节功能评分运动特定子量表(HOS-SSS)、非关节炎髋关节评分(NAHS)、视觉模拟量表(VAS)以及满意度对患者进行术前和术后评估。术后一年,患者报告在疼痛和不稳定方面取得了积极结果。
已有报道称,埃勒斯-当洛综合征患者的肩部和膝部韧带重建取得了积极效果并恢复了稳定性。目前,关于EDS患者接受髋关节手术的文献较少。此外,在正常患者队列中,很少有关于因髋关节不稳定和疼痛而进行圆韧带重建的报道。
这是第一项报道埃勒斯-当洛综合征合并髋关节不稳定患者进行髋关节圆韧带重建的研究。该患者术后1年显示出满意的结果。