Shi Hui, Niu Zhong-Xi, Peng Jun, Yang Yu-Shang, Chen Long-Qi
1 Department of Thoracic Surgery, West China Hospital, Sichuan University, Chengdu 610041, China ; 2 Department of Thoracic Surgery, General Hospital of Chinese People's Armed Police Forces, Beijing 100039, China.
J Thorac Dis. 2015 Mar;7(3):E23-7. doi: 10.3978/j.issn.2072-1439.2015.02.04.
We present an extremely rare case of a giant pulmonary hamartoma (PH) coexisting with an anomalous common pulmonary venous trunk (ACPVT). An asymptomatic 39-year-old man was referred for evaluation of a giant pulmonary lesion in his left thorax detected on chest X-ray during a routine medical examination. After clinical work-up, the patient underwent left exploratory thoracotomy. Since the extent of the tumor and coexistence of an ACPVT, a left pneumonectomy was performed. The specimen measured 28 cm × 18 cm × 17 cm and weighted for 2.1 kg. Histology revealed a blend of pieces of rounded cartilage separated by fibrous bands in which mature adipose tissue and cleft-like structures lined. The features were consistent with those of a chondromatous hamartoma. The patient made a satisfactory recovery and 10 months after the operation was asymptomatic.
我们报告了一例极为罕见的巨大肺错构瘤(PH)合并异常共同肺静脉干(ACPVT)的病例。一名39岁无症状男性在常规体检胸部X线检查时发现左胸有巨大肺部病变,遂转诊进行评估。经过临床检查,患者接受了左开胸探查术。由于肿瘤范围及合并ACPVT,遂行左肺切除术。标本大小为28 cm×18 cm×17 cm,重2.1 kg。组织学检查显示,圆形软骨片被纤维带分隔,其中衬有成熟脂肪组织和裂隙样结构。这些特征与软骨瘤性错构瘤相符。患者恢复良好,术后10个月无症状。