Franco Arie, Gabriel Simon, Ruehm Stefan G
Department of radiology, University of California, Los Angeles, USA.
J Radiol Case Rep. 2014 Nov 30;8(11):25-9. doi: 10.3941/jrcr.v8i11.2277. eCollection 2014 Nov.
The quadricuspid aortic valve is a very rare congenital defect that may be an isolated entity or associated with a multitude of cardiovascular abnormalities. Isolated cases usually manifest late in life with the complication of aortic regurgitation, which can be delayed by early valve replacement. We present a case of quadricuspid aortic valve associated with truncus arteriosus, ventricular septal defect, and interrupted aortic arch.
四叶式主动脉瓣是一种非常罕见的先天性缺陷,可能是孤立存在的,也可能与多种心血管异常相关。孤立病例通常在生命后期因主动脉瓣反流并发症而出现症状,早期进行瓣膜置换可延缓病情发展。我们报告一例四叶式主动脉瓣合并动脉干、室间隔缺损和主动脉弓中断的病例。