Zuberi S A, Liu S, Tam J W, Hussain F, Maguire D, Kass M
Department of Internal Medicine, Faculty of Medicine, University of Manitoba, 409 Tache Avenue, Winnipeg, MB, Canada R2H 2A6.
Section of Cardiology, Department of Internal Medicine, Faculty of Medicine, University of Manitoba, 409 Tache Avenue, Winnipeg, MB, Canada R2H 2A6.
Case Rep Cardiol. 2015;2015:531382. doi: 10.1155/2015/531382. Epub 2015 Apr 7.
Ebstein anomaly is characterized by deformities of the anterior leaflet of the tricuspid valve and atrialization of the right ventricle. Patients with severe tricuspid regurgitation are recommended to have tricuspid valve surgery with concomitant atrial septal defect closure. A 73-year-old female with Ebstein anomaly presented with severe hypoxemia. Transthoracic echocardiography revealed severe tricuspid regurgitation and a patent foramen ovale with right-to-left shunting. Complete percutaneous patent foramen ovale closure led to acute decompensation; however, partial closure led to hemodynamic stability and improved oxygenation. In conclusion, similar patients with "patent foramen ovale dependency" from longstanding shunts may benefit from partial patent foramen ovale closure.
埃布斯坦畸形的特征是三尖瓣前叶畸形和右心室心房化。重度三尖瓣反流患者建议进行三尖瓣手术并同期闭合房间隔缺损。一名73岁患有埃布斯坦畸形的女性出现严重低氧血症。经胸超声心动图显示重度三尖瓣反流和卵圆孔未闭伴右向左分流。经皮完全闭合卵圆孔未闭导致急性失代偿；然而，部分闭合导致血流动力学稳定并改善了氧合。总之，因长期分流而存在“卵圆孔未闭依赖”的类似患者可能从卵圆孔未闭部分闭合中获益。
