Knezevic Srbislav, Ignjatovic Igor, Lukic Snezana, Matic Slavko, Dugalic Vladimir, Knezevic Djordje, Micev Marjan, Dragasevic Sanja
Srbislav Knezevic, Igor Ignjatovic, Slavko Matic, Vladimir Dugalic, Djordje Knezevic, Clinic for Digestive Surgery-First Surgical Clinic, Clinical Center of Serbia, University of Belgrade, 11000 Belgrade, Serbia.
World J Gastroenterol. 2015 May 7;21(17):5427-31. doi: 10.3748/wjg.v21.i17.5427.
Primary retroperitoneal mucinous cystic tumors are extremely rare. These tumors can be classified as a primary retroperitoneal mucinous cystadenoma with or without borderline malignancy or primary retroperitoneal mucinous cystadenocarcinoma. The most common of these is primary retroperitoneal mucinous cystadenoma, which almost always occurs in female patients; only ten cases have been reported in males. The most common clinical findings for this tumor type include nonspecific abdominal pain and a palpable abdominal mass. A definitive diagnosis is usually obtained from histopathology after surgical excision. Here, we report the case of a 60-year-old female patient who complained of abdominal pain that had been present for 3 mo and presented with a palpable abdominal mass. Multidetector computed tomography scanning revealed a large, unilocular cystic mass in the left retroperitoneal space. Surgical intervention was performed and the tumor was completely removed. Histopathologic examination confirmed that the tumor was a primary retroperitoneal mucinous cystadenoma. Two years after surgery, the patient remains disease free.
原发性腹膜后黏液性囊性肿瘤极为罕见。这些肿瘤可分为伴有或不伴有交界性恶性的原发性腹膜后黏液性囊腺瘤或原发性腹膜后黏液性囊腺癌。其中最常见的是原发性腹膜后黏液性囊腺瘤,几乎均发生于女性患者;男性仅报道过10例。该肿瘤类型最常见的临床表现包括非特异性腹痛和可触及的腹部肿块。通常在手术切除后通过组织病理学获得明确诊断。在此,我们报告一例60岁女性患者,主诉腹痛3个月,伴有可触及的腹部肿块。多排螺旋计算机断层扫描显示左腹膜后间隙有一个巨大的单房囊性肿块。进行了手术干预,肿瘤被完全切除。组织病理学检查证实该肿瘤为原发性腹膜后黏液性囊腺瘤。术后两年,患者无疾病复发。