Babu K Anand, Supraja K, Singh Raj B
Indian J Chest Dis Allied Sci. 2014 Oct-Dec;56(4):259-62.
Pulmonary capillary haemangiomatosis (PCH) is a rare disorder of unknown aetiology, characterised by proliferating capillaries that invade the pulmonary interstitium, alveolar septae and the pulmonary vasculature. It is often mis-diagnosed as primary pulmonary hypertension and pulmonary veno-occlusive disease. Pulmonary capillary haemangiomatosis is a locally aggressive benign vascular neoplasm of the lung. We report the case of a 19-year-old female who was referred to us in the early post-partum period with severe pulmonary artery hypertension, which was diagnosed as PCH by open lung biopsy.
肺毛细血管瘤病（PCH）是一种病因不明的罕见疾病，其特征是增殖的毛细血管侵入肺间质、肺泡间隔和肺血管系统。它常被误诊为原发性肺动脉高压和肺静脉闭塞性疾病。肺毛细血管瘤病是一种肺部局部侵袭性良性血管肿瘤。我们报告一例19岁女性病例，该患者在产后早期因严重肺动脉高压转诊至我院，经开胸肺活检诊断为PCH。
