Gotoh T, Hashimoto Y, Araki S, Nakagawa T, Nagata M
Rinsho Shinkeigaku. 1989 Sep;29(9):1156-62.
We reported a 51-year-old male with ischemic disturbance of right inner ear resembling Meniere's disease. The patient had a sudden-onset episode of vertigo, right severe hearing disturbance, nausea, vomiting and gait disturbance. Two days after, he had hypersomnia, vertical gaze palsy, double vision, left Horner's sign, and sensory disturbance of pain and temperature of right half body involving face. Brain MRI disclosed high intensity area in T2-weighted image and proton density in bilateral paramedian thalamo-mesencephalic region and right cerebellum (area of the anterior inferior cerebellar artery). Cerebral angiography showed 90% or more stenosis of the right vertebral artery, 50% stenosis of the left vertebral artery before the posterior inferior cerebellar artery (PICA), and 60% stenosis of distal portion of the basilar artery. Furthermore, stem portion of the posterior cerebral artery, and the right anterior cerebellar artery and the left vertebral artery after the PICA were absent or occluded. Right deafness was evaluated to be Jerger type II, namely disturbance of inner ear. Caloric tests showed no response, and right auditory brainstem response showed no waves. Main cause of this vertigo and right deafness was considered to be disturbance of inner ear due to ischemia of right labyrinthine artery, though this patient was not a typical case of the anterior cerebellar artery syndrome. Ischemic disturbances of inner ear have been reported only in patients with the anterior cerebellar artery syndrome, therefore this patient who had only acute ischemic disturbance of inner ear and did not have disturbance of caudo-lateral portion of the pons was considered to be very rare.
我们报告了一名51岁男性,患有类似梅尼埃病的右内耳缺血性障碍。患者突然发作眩晕、右耳严重听力障碍、恶心、呕吐及步态障碍。两天后,他出现嗜睡、垂直凝视麻痹、复视、左侧霍纳氏征,以及包括面部在内的右半身痛觉和温度觉障碍。脑部MRI显示双侧丘脑正中脑旁区域及右小脑(小脑前下动脉供血区)在T2加权像和质子密度像上有高信号区。脑血管造影显示右椎动脉狭窄90%或以上,左椎动脉在小脑后下动脉(PICA)之前狭窄50%,基底动脉远端狭窄60%。此外,大脑后动脉主干、右小脑前动脉及PICA之后的左椎动脉缺如或闭塞。右耳聋被评估为耶格Ⅱ型,即内耳障碍。冷热试验无反应,右听性脑干反应未引出波。尽管该患者并非典型的小脑前动脉综合征病例,但此次眩晕和右耳聋的主要原因被认为是右迷路动脉缺血导致的内耳障碍。内耳缺血性障碍仅在小脑前动脉综合征患者中被报道过,因此该患者仅有内耳急性缺血性障碍且未出现脑桥尾外侧部障碍,被认为非常罕见。