Asahi Yoshinao, Fujii Ryosuke, Usui Naoko, Kagamiuchi Hajime, Omichi Shiro, Kotani Junichiro
Department of Dentistry, Morinomiya Hospital, Osaka, Japan.
Department of Dentistry, Bobath Memorial Hospital, Osaka, Japan.
Anesth Prog. 2015 Summer;62(2):71-3. doi: 10.2344/0003-3006-62.1.71.
Noonan syndrome (NS) is an autosomal dominant disorder characterized by facial anomalies, short stature, chest deformity, congenital heart diseases, and other comorbidities. The challenges faced during anesthetic management of patients with NS could be due to congenital heart diseases, hemostatic disorders, and airway anomalies. Here we describe dental treatment under general anesthesia performed for a 28-year-old man with NS. He had characteristic features of NS along with mild pulmonary valve stenosis. Dental treatment under general anesthesia was performed successfully on 13 occasions with nasotracheal intubation under curve-tipped suction catheter guidance or insertion of a reinforced laryngeal mask airway. This case suggests that for patients with NS, who might present several challenges, dental anesthesiologists should consider the extent of the patient's disorders to enable them to perform dental treatment safely under general anesthesia.
努南综合征（NS）是一种常染色体显性疾病，其特征为面部异常、身材矮小、胸部畸形、先天性心脏病及其他合并症。NS患者麻醉管理过程中面临的挑战可能源于先天性心脏病、止血障碍和气道异常。在此，我们描述了一名28岁NS男性患者在全身麻醉下接受的牙科治疗。他具有NS的典型特征以及轻度肺动脉瓣狭窄。在弯头吸引导管引导下经鼻气管插管或插入加强型喉罩气道，成功地在全身麻醉下进行了13次牙科治疗。该病例表明，对于可能存在多种挑战的NS患者，牙科麻醉医生应考虑患者疾病的程度，以便能够在全身麻醉下安全地进行牙科治疗。
