先天性外淋巴瘘：一种被忽视的诊断？

Congenital perilymphatic fistula: an overlooked diagnosis?

作者信息

Reilly J S, Kenna M A

机构信息

University of Alabama, Birmingham.

出版信息

Am J Otol. 1989 Nov;10(6):496-8. doi: 10.1097/00129492-198911000-00018.

DOI:10.1097/00129492-198911000-00018

PMID:2610243

Abstract

Congenital perilymphatic fistula (CPLF) often is the sole cause of sensorineural hearing loss in children that is both progressive and subtle and, therefore, can elude detection by physicians. A 3-year prospective study of 244 children with sensorineural hearing loss of unknown etiology demonstrated that at least 6% (15/244) had CPLF. Close audiologic monitoring and radiologic imaging of the temporal bone of children with sensorineural hearing loss are recommended to detect CPLF.

摘要

先天性外淋巴瘘（CPLF）通常是儿童感音神经性听力损失的唯一原因，这种听力损失具有渐进性且不易察觉，因此医生可能难以发现。一项针对244例病因不明的感音神经性听力损失儿童的为期3年的前瞻性研究表明，至少6%（15/244）的患儿患有CPLF。建议对感音神经性听力损失儿童进行密切的听力学监测和颞骨影像学检查，以检测CPLF。