Doksöz Önder, Terek Demet Tümay, Karaçelik Mustafa, Yıldırım Hülya Tosun, Demirağ Bengü, Meşe Timur, Sarıosmanoğlu Osman Nejat, Arslanoğlu Sertaç
Departments of Pediatric Cardiology.
Neonatology.
Pediatr Int. 2015 Oct;57(5):968-70. doi: 10.1111/ped.12655. Epub 2015 Jul 6.
Primary cardiac tumor is uncommon in childhood, with an incidence of 0.06-0.32%, and intrapericardial teratoma represents an exceptional rarity among these entities. Germ cell tumors (GCT) are rare, representing only 1-3% of childhood tumors. Twenty per cent of GCT are malignant and are associated with age and location. Extragonadal involvement accounts for nearly half of the cases. Anterior mediastinum is a common location of malignant germ cell tumors, yet pericardial and aortic adventitia involvement have been rarely reported. Here we report the case of a preterm twin baby boy with intrapericardial mixed germ cell tumor who presented with hydrops fetalis and pericardial effusion.
原发性心脏肿瘤在儿童时期并不常见,发病率为0.06%-0.32%,而心包内畸胎瘤在这些肿瘤中极为罕见。生殖细胞肿瘤(GCT)很少见,仅占儿童肿瘤的1%-3%。20%的GCT是恶性的,且与年龄和部位有关。性腺外受累约占病例的一半。前纵隔是恶性生殖细胞肿瘤的常见部位,但心包和主动脉外膜受累的报道很少。在此,我们报告一例患有心包内混合性生殖细胞肿瘤的早产双胞胎男婴,其表现为胎儿水肿和心包积液。