Ohyama Kaname, Baba Miyako, Tamai Mami, Yamamoto Motohisa, Ichinose Kunihiro, Kishikawa Naoya, Takahashi Hiroki, Kawakami Atsushi, Kuroda Naotaka
a Course of Pharmaceutical Sciences, Graduate School of Biomedical Sciences, Nagasaki University , Nagasaki , Japan.
b Nagasaki University Research Centre for Genomic Instability and Carcinogenesis (NRGIC) , Nagasaki , Japan.
Mod Rheumatol. 2016;26(2):248-50. doi: 10.3109/14397595.2015.1072296. Epub 2015 Aug 18.
IgG4-related disease (IgG4-RD) is characterized by various serological abnormalities. Some patients with IgG4-RD present with hypergammaglobulinemia, hypocomplementemia, and autoantibodies recognizing rheumatoid factors and nuclear factors. However, whether IgG4-RD is an autoimmune disease remains unclear.
Here, we used immune complexome analysis to comprehensively identify constituent antigens of circulating immune complexes isolated from 10 patients with IgG4-related dacryoadenitis and/or sialadenitis (IgG4-RDS) which is one condition associated with IgG4-RD.
We detected each of 125 distinct antigens in independent samples from two or more patients with IgG4-RDS. Of them, 17 antigens were found to be specific to patients with IgG4-RDS by comparing 125 antigens with all the antigens found in other connective tissue diseases (antineutrophil cytoplasmic antibody-associated vasculitis, Takayasu's arteritis, mixed connective tissue disease, dermatomyositis, Sjögren's syndrome, systemic scleroderma, and systemic lupus erythematosus) or healthy donors. The number of disease-specific antigens associated with IgG4-RDS was comparable to those autoimmune diseases.
Studies of the 17 IgG4-RDS-specific antigens might lead to a better understanding of the pathogenesis of IgG4-RD, but further study of the prevalence of these CIC-associated antigens that involves a selective and sensitive assay will be needed to determine their potential as diagnostic or pathogenic biomarkers.
IgG4相关疾病(IgG4-RD)具有多种血清学异常特征。一些IgG4-RD患者表现为高球蛋白血症、低补体血症以及可识别类风湿因子和核因子的自身抗体。然而,IgG4-RD是否为自身免疫性疾病仍不明确。
在此,我们采用免疫复合物组分析,全面鉴定从10例IgG4相关泪腺炎和/或涎腺炎(IgG4-RDS,这是一种与IgG4-RD相关的病症)患者中分离出的循环免疫复合物的组成抗原。
我们在来自两名或更多IgG4-RDS患者的独立样本中检测到了125种不同的抗原。通过将这125种抗原与在其他结缔组织疾病(抗中性粒细胞胞浆抗体相关性血管炎、大动脉炎、混合性结缔组织病、皮肌炎、干燥综合征、系统性硬化症和系统性红斑狼疮)或健康供体中发现的所有抗原进行比较,发现其中17种抗原是IgG4-RDS患者所特有的。与IgG4-RDS相关的疾病特异性抗原数量与那些自身免疫性疾病相当。
对这17种IgG4-RDS特异性抗原的研究可能有助于更好地理解IgG4-RD的发病机制,但需要进一步研究这些与循环免疫复合物相关抗原的普遍性,这涉及一种选择性和敏感性检测方法,以确定它们作为诊断或致病生物标志物的潜力。