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一名患有多克隆免疫母细胞增多症的儿童先后出现免疫性全血细胞减少症和新发弥散性血管内凝血。

Sequential occurrence of immune pancytopenia and de novo DIC in a child with polyclonal immunoblastosis.

作者信息

Hanada T, Mori N, Nakahara S, Ehara T, Iwasaki N, Kataoka N, Saito K, Takita H

出版信息

Nihon Ketsueki Gakkai Zasshi. 1989 Jul;52(4):778-84.

PMID:2618552
Abstract

We report a child with polyclonal immunoblastosis associated with several hematological complications. Pure red cell aplasia (IgG-mediated inhibition of erythropoiesis), immune thrombocytopenia and immune neutropenia with myeloid hypoplasia developed sequentially. In addition, disseminated intravascular coagulation occurred shortly after the administration of prednisolone with rapid shrinkage of hepatosplenomegaly and lymphadenopathy.

摘要

我们报告了一名患有多克隆免疫母细胞增多症并伴有多种血液学并发症的儿童。相继出现了纯红细胞再生障碍性贫血(IgG介导的红细胞生成抑制)、免疫性血小板减少症以及伴有骨髓发育不全的免疫性中性粒细胞减少症。此外,在给予泼尼松龙后不久发生了弥散性血管内凝血,同时肝脾肿大和淋巴结病迅速缩小。

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1
Sequential occurrence of immune pancytopenia and de novo DIC in a child with polyclonal immunoblastosis.一名患有多克隆免疫母细胞增多症的儿童先后出现免疫性全血细胞减少症和新发弥散性血管内凝血。
Nihon Ketsueki Gakkai Zasshi. 1989 Jul;52(4):778-84.
2
De novo disseminated intravascular coagulation in angioimmunoblastic lymphadenopathy (AILD).血管免疫母细胞性淋巴结病(AILD)中的新发弥散性血管内凝血。
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