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一例罕见的库斯莫尔病(纤维蛋白性涎腺炎)。

A rare case of Kussmaul Disease (Sialodochitis Fibrinosa).

作者信息

Ray Amrita, Burgin Sarah J, Spector Matthew E

机构信息

University of Michigan Health System, Department of Otolaryngology-Head and Neck Surgery, Ann Arbor, Michigan.

出版信息

J Case Rep Med. 2015;4(1+3). doi: 10.4303/jcrm/235894.

Abstract

Sialodochitis fibrinosa (or commonly known as Kussmaul Disease) is a rare salivary gland disease characterized by recurrent salivary gland swelling and pain as a result of mucofibrinous plugs. Typically patients have a history of multiply recurrent glandular swelling, dehydration and/or decreased salivary flow, thick secretions from Stensen's or Wharton's duct, and/or history of allergic diseases. Retention of mucofibrinous plugs may lead to acute suppurative parotitis and chronic sialadenitis ultimately. The diagnosis is one of exclusion, and treatment is based on symptomatology and largely supportive.

摘要

纤维蛋白性涎管炎(通常称为库斯莫尔病)是一种罕见的唾液腺疾病,其特征是由于黏液纤维蛋白栓导致唾液腺反复肿胀和疼痛。典型的患者有多次复发性腺体肿胀、脱水和/或唾液分泌减少、腮腺导管或颌下腺导管浓稠分泌物以及/或过敏性疾病史。黏液纤维蛋白栓的潴留最终可能导致急性化脓性腮腺炎和慢性涎腺炎。诊断是排除性诊断之一,治疗基于症状,主要是支持性治疗。

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本文引用的文献

1
Allergic parotitis.
J Allergy. 1947 Jan;18(1):51-4. doi: 10.1016/0021-8707(47)90067-1.
3
Submandibular salivary disease: a proposed allergic aetiology.
J Laryngol Otol. 1995 Jan;109(1):66-7. doi: 10.1017/s0022215100129275.

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