Merard Reena, Ganesan Raji, Hirschowitz Lynn
Department of Cellular Pathology, Birmingham Women's Hospital, Birmingham, United Kingdom.
Int J Gynecol Pathol. 2015 Sep;34(5):465-72. doi: 10.1097/PGP.0000000000000180.
We report 2 cases of growing teratoma syndrome (GTS) in patients who had been treated with surgery and chemotherapy for immature ovarian teratoma. One of the patients presented with probable paraneoplastic encephalitis. Resection of "recurrences" in both patients showed deposits of mature teratoma and extensive gliomatosis peritonei. It is important for both pathologists and clinicians to be aware of this uncommon entity to avoid misdiagnosis of GTS as recurrence of immature teratoma and disease progression, and to avert unnecessary continuation of chemotherapy. GTS may occur several years after diagnosis of the primary tumor, and rarely develop in treated patients who have become pregnant. Surgical debulking is the optimal modality of treatment as GTS is not chemosensitive. If surgical debulking of GTS is incomplete, long-term follow-up with imaging is required to avoid complications such as bowel obstruction and the sequelae of pressure effects (such as vascular thrombosis, fistula formation, etc.) from bulky deposits of mature teratoma/GTS and gliomatosis peritonei.
我们报告了2例生长性畸胎瘤综合征(GTS)患者,这2例患者曾接受过手术及化疗以治疗未成熟卵巢畸胎瘤。其中1例患者表现为可能的副肿瘤性脑炎。对2例患者“复发灶”的切除显示有成熟畸胎瘤沉积物及广泛的腹膜胶质瘤病。病理学家和临床医生都应了解这一罕见实体,以避免将GTS误诊为未成熟畸胎瘤复发及疾病进展,并避免不必要地继续化疗。GTS可能在原发性肿瘤诊断数年之后发生,且很少在已怀孕的接受治疗患者中出现。手术减瘤是最佳治疗方式,因为GTS对化疗不敏感。如果GTS的手术减瘤不完全,则需要长期影像学随访,以避免诸如肠梗阻以及成熟畸胎瘤/GTS大量沉积物和腹膜胶质瘤病的压迫效应后遗症(如血管血栓形成、瘘管形成等)等并发症。