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[腹外脐静脉静脉曲张。病例报告]

[Extra-abdominal umbilical vein varix. A case report].

作者信息

Soriano-Lillo Paula, Padilla-V Carmen, Blázquez-R Ana Rosa, Crespo V

出版信息

Ginecol Obstet Mex. 2015 Jun;83(6):356-62.

PMID:26285487
Abstract

UNLABELLED

The intra-abdominal umbilical vein varix is very uncommon, characterized by a dilation of the vein, usually located between its entry into the abdomen and completion in the portal system. However, the location of this anomaly to extra-abdominal level is very unusual and more difficult to diagnose by ultrasound.

CLINICAL CASE

We present a case undiagnosed during pregnancy, demonstrating cord abnormality in its extra-abdominal portion and confirmed later by the pathology study. It was a gestation of 36 + 6 weeks, ending by performing emergency caesarean section for abnormal fetal heart rate, with good perinatal outcome. The diagnosis was made after placental delivery, by the existence of fibrotic cystic structure in the middle third of the umbilical cord.

摘要

未标注

腹内脐静脉静脉曲张非常罕见,其特征为静脉扩张,通常位于其进入腹部处至门静脉系统汇入处之间。然而,这种异常位于腹外水平的情况非常少见,且通过超声更难诊断。

临床病例

我们报告一例在孕期未被诊断出的病例,该病例显示脐带腹外部分存在异常,后经病理研究得以证实。这是一例孕36 + 6周的妊娠,因胎儿心率异常行急诊剖宫产结束妊娠,围产期结局良好。胎盘娩出后,通过脐带中三分之一处存在纤维化囊性结构作出诊断。

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1
[Extra-abdominal umbilical vein varix. A case report].[腹外脐静脉静脉曲张。病例报告]
Ginecol Obstet Mex. 2015 Jun;83(6):356-62.
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Severe fetal anemia as a consequence of extra-abdominal umbilical vein varix: A case report and review of the literature.胎儿严重贫血为腹部外脐静脉静脉瘤所致:病例报告及文献复习。
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