Guan Zhe, Hollon Todd, Bentley J Nicole, Garton Hugh J L
University of Michigan Medical School; and.
Department of Neurosurgery, University of Michigan Health System, Ann Arbor, Michigan.
J Neurosurg Pediatr. 2015 Nov;16(5):574-578. doi: 10.3171/2015.4.PEDS153. Epub 2015 Aug 21.
Epidermoid cysts (ECs) are uncommon pediatric tumors that often occur in the cerebellopontine angle. Although cyst rupture is a recognized complication, the radiographic evolution of an EC following rupture and the resultant parenchymal brainstem edema have not been reported. The authors present the case of a 13-year-old female with a newly diagnosed cerebellopontine angle EC who presented with worsening headaches, photophobia, and emesis. Magnetic resonance imaging demonstrated significant pericystic brainstem edema and mass effect with effacement of the fourth ventricle. Refractory symptoms prompted repeat imaging, revealing cyst enlargement and dense rim enhancement. Resection of the EC resolved both her symptoms and the brainstem edema. This case documents the radiographic evolution of EC rupture and subsequent clinical course.