肺淋巴管平滑肌瘤病——病例报告

Pulmonary lymphangioleiomyomatosis--a case report.

作者信息

Li Chun-Jie, Gao Guo-Zheng, Xu Meilin, Fan Guan-Wei

机构信息

Department of Pathology, Tianjin Chest Hospital, Tianjin, China.

Institute of Traditional Chinese Medicine Research, Tianjin State Key Laboratory of Modern Chinese Medicine, Tianjin University of Traditional Chinese Medicine, Tianjin 300193, China.

出版信息

J Cancer Res Ther. 2015 Aug;11 Suppl 1:C138-9. doi: 10.4103/0973-1482.163875.

DOI:10.4103/0973-1482.163875

PMID:26323915

Abstract

Pulmonary lymphangioleiomyomatosis (PLAM) is a rare disease, occurs in 16-68-year-old women, especially in women of childbearing age. High-resolution computed tomography would be useful for diagnosis of PLAM. Immunohistochemistry of smooth muscle actin (SMA) and HMB-45 smooth muscle cells was positive for smooth muscle cells. Progesterone receptor and estrogen receptor in some smooth muscle cells were positive for some smooth muscle cells. HMB-45-positive diagnosis of the disease is more important.

摘要

肺淋巴管平滑肌瘤病（PLAM）是一种罕见疾病，发生于16至68岁的女性，尤其是育龄女性。高分辨率计算机断层扫描对PLAM的诊断有帮助。平滑肌肌动蛋白（SMA）和HMB - 45平滑肌细胞的免疫组织化学检查显示平滑肌细胞呈阳性。部分平滑肌细胞中的孕激素受体和雌激素受体呈阳性。对该疾病进行HMB - 45阳性诊断更为重要。