Pei Guoyuan, Yang Dan, Sun Jiayu, Luo Yong, Yan Jiaqi, Chen Yucheng
Division of Cardiology, West China Hospital, Sichuan University.
Int Heart J. 2015;56(5):571-3. doi: 10.1536/ihj.15-038. Epub 2015 Sep 4.
We present a case of POEMS syndrome in which cardiac MRI (CMR) revealed cardiac involvement. POEMS syndrome is a very rare disease and cardiac involvement in POEMS syndrome is rarely reported. In the present case, echocardiography revealed left ventricular hypertrophy with moderately impaired systolic function and moderate pulmonary hypertension. CMR examination showed a typical circular subendocardial type of late gadolinium enhancement, which is a classic pattern of cardiac amyloidosis. The diagnosis of cardiac amyloidosis in POEMS would be helpful for further risk stratification and treatment strategies.