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一名患有法洛四联症儿童的肾病综合征:一种罕见的关联。

Nephrotic Syndrome in a Child Suffering from Tetralogy of Fallot: A Rare Association.

作者信息

Ekulu Pépé Mfutu, Kazadi-Wa-Kazadi Orly, Lumbala Paul Kabuyi, Aloni Michel Ntetani

机构信息

Division of Paediatric Haemato-Oncology and Nephrology, Department of Paediatrics, University Hospital of Kinshasa, Faculty of Medicine, University of Kinshasa, Kinshasa, Congo.

Division of Cardiology, Department of Paediatrics, University Hospital of Kinshasa, Faculty of Medicine, University of Kinshasa, Kinshasa, Congo.

出版信息

Case Rep Pediatr. 2015;2015:128409. doi: 10.1155/2015/128409. Epub 2015 Aug 3.

Abstract

Nephrotic syndrome is an uncommon complication of tetralogy of Fallot and has been rarely reported in pediatric population. We describe a 4-year-old female Congolese child who was referred for investigation for persistent dyspnea, edema, and cyanosis and nephrotic range proteinuria. Our patient presented with a tetralogy of Fallot and nephrotic syndrome. Conclusion. This case reminds us that children with tetralogy of Fallot may develop nephrotic proteinuria.

摘要

肾病综合征是法洛四联症一种不常见的并发症,在儿科人群中鲜有报道。我们描述了一名4岁刚果女童,因持续呼吸困难、水肿、发绀及肾病范围蛋白尿前来接受检查。我们的患者患有法洛四联症和肾病综合征。结论。该病例提醒我们,法洛四联症患儿可能会出现肾病性蛋白尿。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/fb48/4548070/3b23e723d36a/CRIPE2015-128409.001.jpg

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