Feki A, Haag R, Warter A
Actual Odontostomatol (Paris). 1989 Sep;43(167):551-62.
A new case of basal cell naevomatosis, localized in the jaws as odontogenic keratocysts, is described and the importance of the diagnostic role plaid by the dentist is underlined. Skin lesions, bone involvements and the hereditary character of the disease are described. Special emphasis is given to the importance and the easy accessibility of the oral manifestations. Possible evolution towards advanced forms, and the heterogeneity of the symptoms lay the stress on the need of an early diagnosis and the necessity of a close collaboration with the various specialists concerned.
本文描述了一例基底细胞痣综合征新病例,病变局限于颌骨,表现为牙源性角化囊肿,并强调了牙医在诊断中的重要作用。文中还描述了该疾病的皮肤病变、骨受累情况及其遗传特征。特别强调了口腔表现的重要性及易于观察到。疾病可能向晚期发展,症状具有异质性,这凸显了早期诊断的必要性以及与相关各科专家密切合作的必要性。