M Allmendinger Andrew, A Ricci Joseph, S Desai Naman, Viswanadhan Narayan, Rodriguez Diana
The Department of Radiology, Brigham and Women's Hospital, Harvard Medical School, Boston, MA, USA.
The Division of Plastic Surgery, Brigham and Women's Hospital, Harvard Medical School, Boston, MA, USA.
Iran J Child Neurol. 2015 Summer;9(3):62-8.
Linear scleroderma "en coup de sabre" is a subset of localized scleroderma with band-like sclerotic lesions typically involving the fronto-parietal regions of the scalp. Patients often present with neurologic symptoms. On imaging, patients may have lesions in the cerebrum ipsilateral to the scalp abnormality. Infratentorial lesions and other lesions not closely associated with the overlying scalp abnormality, such as those found in the cerebellum, have been reported, but are extremely uncommon. We present a case of an 8-year-old boy with a left fronto-parietal "en coup de sabre" scalp lesion and describe the neuroimaging findings of a progressively enlarging left cerebellar lesion discovered incidentally on routine magnetic resonance imaging. Interestingly, the patient had no neurologic symptoms given the size of the mass identified.
线状硬皮病“剑伤样”是局限性硬皮病的一个亚型，其带状硬化性病变通常累及头皮的额顶区域。患者常出现神经症状。影像学检查时，患者在头皮异常同侧的大脑可能有病变。幕下病变以及其他与上方头皮异常无密切关联的病变，如在小脑发现的病变，虽有报道，但极为罕见。我们报告一例8岁男孩，其左侧额顶有“剑伤样”头皮病变，并描述了在常规磁共振成像时偶然发现的左侧小脑病变逐渐增大的神经影像学表现。有趣的是，鉴于所发现肿块的大小，该患者并无神经症状。
