Amir Ida, Crow Yanick J, Morar Pradeep
Department of Otolaryngology-Head and Neck Surgery, NHS Lothian, Lauriston Place, Edinburgh EH3 9HA, UK.
Ear Nose Throat J. 2015 Sep;94(9):E1-3.
We describe the cases of 2 brothers in their early 50s, born to consanguineous parents, who presented with acute stridor as a result of adult-onset bilateral abductor vocal fold paralysis. Both patients had a history of adult-onset asthma. No other associated symptoms were evident, and findings on neurologic examination and all other investigations were normal. Both patients required emergency surgical tracheostomy. Another brother with a similar history had died of an airway problem when he was 53 years of age; 2 other younger brothers and 3 younger sisters were currently unaffected. To the best of our knowledge, this is the first report of adult-onset familial bilateral vocal fold paralysis in the absence of associated features. The parents' consanguinity suggested an autosomal recessive basis to this disorder. In addition to describing the features of this case, we review the literature relating to adult-onset familial vocal fold paralysis.
我们描述了一对50岁出头的兄弟的病例,他们的父母是近亲结婚。这两名患者因成人期双侧声带外展麻痹而出现急性喘鸣。两名患者都有成人期哮喘病史。未发现其他相关症状,神经系统检查及所有其他检查结果均正常。两名患者均需要紧急手术气管切开术。另一名有类似病史的兄弟在53岁时死于气道问题;另外两名弟弟和三名妹妹目前未受影响。据我们所知,这是首例无相关特征的成人期家族性双侧声带麻痹报告。父母的近亲关系提示该疾病为常染色体隐性遗传。除了描述该病例的特征外,我们还回顾了与成人期家族性声带麻痹相关的文献。