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小儿重型β地中海贫血伴脾功能亢进行脾切除术的麻醉管理：4例报告

Anaesthetic management of beta thalassemia major with hypersplenism for splenectomy in pediatric age group: Report of four cases.

作者信息

Jyothi B, Sushma K S, Syeda Seham, Raza Syed Owais

机构信息

Department of Anaesthesiology, KIMS, Hubli, Karnataka, India.

出版信息

Anesth Essays Res. 2015 May-Aug;9(2):266-9. doi: 10.4103/0259-1162.156362.

DOI:10.4103/0259-1162.156362
PMID:26417142
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC4563969/
Abstract

Beta thalassemia is the most common cause of hemolytic anemia in India. Hereby we are reporting four cases of beta thalassemia major aged between 5 and 10 years posted for splenectomy over a period of 2 months. These patients were on repeated blood transfusions since the day of diagnosis, and two patients had a history of cardiac failure. In addition to emphasizing the anesthetic challenges, the purpose of reporting such cases is to raise the awareness of the disease and prevention of the same by aggressive screening and prenatal diagnosis.

摘要

β地中海贫血是印度溶血性贫血最常见的病因。在此，我们报告4例年龄在5至10岁之间的重型β地中海贫血患者，在2个月的时间里接受了脾切除术。这些患者自确诊之日起就反复输血，其中2例有心力衰竭病史。除了强调麻醉方面的挑战外，报告此类病例的目的是提高对该疾病的认识，并通过积极筛查和产前诊断预防该疾病。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f494/4563969/914980aaf63f/AER-9-266-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f494/4563969/914980aaf63f/AER-9-266-g001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/f494/4563969/914980aaf63f/AER-9-266-g001.jpg

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Haemoglobinopathies in southeast Asia.东南亚的血红蛋白病。
Indian J Med Res. 2011 Oct;134(4):498-506.
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Anaesthetic management of a patient with Eisenmenger syndrome and β-thalassemia major for splenectomy.艾森曼格综合征合并重型β地中海贫血患者行脾切除术的麻醉管理
Indian J Anaesth. 2011 Mar;55(2):187-9. doi: 10.4103/0019-5049.79892.
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Thalassemia: an overview of 50 years of clinical research.地中海贫血：50 年临床研究综述。
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