Chen Bo-Jung, Chang Sheng-Tsung, Weng Shih-Feng, Huang Wan-Ting, Chu Pei-Yi, Hsieh Pin-Pen, Jung Yun-Chih, Kuo Chun-Chi, Chuang Yu-Ting, Chuang Shih-Sung
a Department of Pathology , Shuang Ho Hospital, Taipei Medical University , New Taipei City , Taiwan .
b Department of Pathology , Chi-Mei Medical Center , Tainan , Taiwan .
Leuk Lymphoma. 2016;57(3):644-53. doi: 10.3109/10428194.2015.1076928. Epub 2015 Sep 30.
This study retrospectively investigated 54 cases of sporadic Burkitt lymphoma in Taiwan with histopathology review, immunohistochemistry, Epstein-Barr virus (EBV) in situ hybridization (EBER) and fluorescence in situ hybridization (FISH). The great majority revealed typical immunophenotype and 89% (47/53) cases expressed myc protein. EBER was positive in 20% (11/54) of cases, more frequently with nodal presentation, but not significantly associated with age (pediatric vs. adult), abdominal vs. extra-abdominal presentation or overall survival (OS). MYC and IGH were rearranged in 94% (46/49) and 85% (41/48) of cases, respectively. The concordance rate between myc expression and MYC translocation was 83% (40/48). By univariate analysis, OS was statistically associated with age, with or without chemotherapy, central nervous system (CNS) involvement, CNS prophylaxis and leukemic transformation, but not gender, nodal vs. extranodal involvement, stage, immunohistochemistry, EBER, myc expression, MYC translocation or radiotherapy. By multivariate analysis, CNS involvement at presentation and administration of chemotherapy were statistically associated with OS.
本研究回顾性调查了台湾地区54例散发性伯基特淋巴瘤患者,进行了组织病理学检查、免疫组化、爱泼斯坦-巴尔病毒(EBV)原位杂交(EBER)及荧光原位杂交(FISH)。绝大多数病例显示典型免疫表型,89%(47/53)的病例表达myc蛋白。20%(11/54)的病例EBER呈阳性,更常见于淋巴结受累情况,但与年龄(儿童与成人)、腹部与腹部外受累表现或总生存期(OS)无显著相关性。MYC和IGH分别在94%(46/49)和85%(41/48)的病例中发生重排。myc表达与MYC易位之间的一致率为83%(40/48)。单因素分析显示,总生存期与年龄、是否接受化疗、中枢神经系统(CNS)受累、CNS预防及白血病转化具有统计学相关性,但与性别、淋巴结与结外受累、分期、免疫组化、EBER、myc表达、MYC易位或放疗无关。多因素分析显示,初诊时CNS受累及化疗的应用与总生存期具有统计学相关性。