奥蒙德病——IgG4相关性疾病。

Ormond's Disease--IgG4-related Disease.

作者信息

Průcha Miroslav, Kolombo Ivan, Štádler Petr

机构信息

Department of Clinical Biochemistry, Haematology and Immunology, Na Homolce Hospital, Prague, Czech Republic.

Department of Urology, Third Faculty of Medicine, Charles University in Prague and University Hospital Královské Vinohrady, Prague, Czech Republic.

出版信息

Prague Med Rep. 2015;116(3):181-92. doi: 10.14712/23362936.2015.57.

DOI:10.14712/23362936.2015.57

PMID:26445389

Abstract

Ormond's disease is a relatively rare disease with unclear etiology, characterized by chronic periaortitis and retroperitoneal fibrosis. The inflammatory process affects the infrarenal part of the abdominal aorta and the iliac arteries, and the presence of infiltrates encasing the ureters and inferior vena cava. This disease is currently classed as an IgG4-related disease. In our review we analyse the clinical history, diagnostic approaches, surgical and immunosuppressive therapies.

摘要

奥蒙德病是一种病因不明的相对罕见疾病，其特征为慢性主动脉周炎和腹膜后纤维化。炎症过程累及腹主动脉肾下段和髂动脉，并出现包裹输尿管和下腔静脉的浸润灶。该疾病目前被归类为IgG4相关性疾病。在我们的综述中，我们分析了临床病史、诊断方法、手术及免疫抑制治疗。