对脆性X综合征男童的重复行为进行特征描述。
Characterising repetitive behaviours in young boys with fragile X syndrome.
作者信息
Oakes A, Thurman A J, McDuffie A, Bullard L M, Hagerman R J, Abbeduto L
机构信息
MIND Institute, University of California Davis, Sacramento, CA, USA.
出版信息
J Intellect Disabil Res. 2016 Jan;60(1):54-67. doi: 10.1111/jir.12234. Epub 2015 Oct 8.
BACKGROUND
Repetitive behaviours are frequently observed in individuals with intellectual disability (ID). The present study examined the profile, inter-correlations and predictive correlates of repetitive behaviours in boys with fragile X syndrome (FXS), the leading inherited cause of ID. Specific child characteristics examined as predictors included anxiety, nonverbal cognition and autism social-affective symptomatology.
METHOD
Participants were 39 boys with FXS (aged 6-10 years). Repetitive behaviours were measured using the Repetitive Behavior Scale - Revised (RBS-R) - a 43-item caregiver-report measure normed on individuals with ID.
RESULTS
Restricted Interests and Sensory Motor behaviours were reported as most problematic for this sample of boys, whereas Self-injurious behaviours were less problematic. All subscales of the RBS-R were significantly inter-correlated. Nonverbal IQ was negatively related, whereas anxiety and social affective symptoms of autism spectrum disorder were positively related, to scores for Restricted Interests. Anxiety was also positively related to scores for Compulsive behaviours and Ritualistic Sameness behaviours.
CONCLUSIONS
This study provides a preliminary description of repetitive behaviours in boys with FXS, which may form the groundwork for future research.
背景
在智力障碍（ID）个体中经常观察到重复行为。本研究调查了脆性X综合征（FXS）男孩重复行为的特征、相互关系和预测相关因素，FXS是ID的主要遗传性病因。作为预测因素进行研究的特定儿童特征包括焦虑、非语言认知和自闭症社会情感症状。
方法
参与者为39名患有FXS的男孩（年龄6至10岁）。使用修订版重复行为量表（RBS-R）测量重复行为，这是一项43项的照顾者报告测量工具，以ID个体为常模。
结果
对于这个男孩样本，兴趣受限和感觉运动行为被报告为问题最大，而自伤行为问题较小。RBS-R的所有子量表都显著相互关联。非语言智商与兴趣受限得分呈负相关，而自闭症谱系障碍的焦虑和社会情感症状与兴趣受限得分呈正相关。焦虑也与强迫行为和仪式性相同行为得分呈正相关。
结论
本研究对FXS男孩的重复行为进行了初步描述，这可能为未来的研究奠定基础。
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