Andrade Gabriel Costa de, Pinto Neviçolino Pereira de Carvalho, Motono Márcia, Chojniak Martha Motono, Chojniak Rubens, Bezerra Stephania Martins
Ophtalmology Department, Hospital A. C. Camargo, São Paulo, SP, BR.
Pediatrics Department, Hospital A.C.Camargo, São Paulo, SP, BR.
Rev Assoc Med Bras (1992). 2015 Aug;61(4):308-10. doi: 10.1590/1806-9282.61.04.308.
Retinoblastomas (RB) are the main forms of intraocular tumor in childhood, with a worldwide incidence of 1 case per 15,000 to 20,000 live births. Trilateral RB (RBT) is a rare combination of unilateral or bilateral RB with a midline intracranial neoplasm of neuroblastic origin, usually found in the pineal region or the suprasellar region, presenting variable incidence of 0.5% up to 6% among patients with RB. The article reports a case of unilateral RBT in a patient treated at Hospital A.C.Camargo.
视网膜母细胞瘤(RB)是儿童眼内肿瘤的主要形式,全球发病率为每15,000至20,000例活产中有1例。三侧性视网膜母细胞瘤(RBT)是一种罕见的单侧或双侧RB与神经母细胞源性中线颅内肿瘤的组合,通常见于松果体区或鞍上区,在RB患者中的发病率为0.5%至6%不等。本文报道了在A.C.卡马戈医院接受治疗的一名单侧RBT患者的病例。