Manuel Valdano, Sousa-Uva Miguel, Morais Humberto, Magalhães Manuel P, Pedro Albino, Miguel Gade, Nunes Maria A S, Gamboa Sebastiana, Júnior António P F
Cardio-Thoracic Center, Clínica Girassol, Luanda, Angola
Cardio-Thoracic Center, Clínica Girassol, Luanda, Angola Hospital Cruz Vermelha, Lisbon, Portugal.
World J Pediatr Congenit Heart Surg. 2015 Oct;6(4):521-5. doi: 10.1177/2150135115601832.
Anomalous origin of one pulmonary artery is a rare congenital heart disease in which one pulmonary artery branch originates from the ascending aorta.
To describe the experience of a cardiothoracic center in an African country to repair anomalous origin of one pulmonary artery in the context of Portugal-Angola collaboration.
Between March 2011 and March 2015, four consecutive patients with anomalous origin of pulmonary artery branch underwent surgical correction. The mean age was 1.6 months. The mean weight was 4 kg. All had right pulmonary artery branch originating from the ascending aorta. All patients underwent direct implantation of right pulmonary branch to main pulmonary artery. Two patents had patent ductus arteriosus and one had atrial septal defect. Two patients had pulmonary hypertension.
There was no registration of death. The mean cardiopulmonary bypass time was 75.5 ± 4.5 minutes, mean aortic cross-clamping time was 40 ± 5.6 minutes, and mean duration of the postoperative intensive care unit stay was 6.8 ± 5.7 days. At discharge, one patient had residual gradient of 25 mm Hg, the remainder had no significant gradient. The mean follow-up time was 11 months (5-28 months). One week after discharge, one patient presented operative wound dehiscence. At the last follow-up, all patients were alive, and no significant residual gradient or stenosis at site of anastomosis was observed. No reintervention was required.
Anomalous origin of one pulmonary artery is a rare but potentially treatable lesion if operated early in life. Direct implantation was a good technique with good short-term results.
一侧肺动脉起源异常是一种罕见的先天性心脏病,其中一侧肺动脉分支起源于升主动脉。
描述一个非洲国家心胸中心在葡萄牙 - 安哥拉合作背景下修复一侧肺动脉起源异常的经验。
2011年3月至2015年3月期间,对4例连续的肺动脉分支起源异常患者进行了手术矫正。平均年龄为1.6个月。平均体重为4千克。所有患者均为右肺动脉分支起源于升主动脉。所有患者均接受了右肺动脉分支直接植入主肺动脉手术。2例患者有动脉导管未闭,1例有房间隔缺损。2例患者有肺动脉高压。
无死亡记录。平均体外循环时间为75.5±4.5分钟,平均主动脉阻断时间为40±5.6分钟,术后重症监护病房平均住院时间为6.8±5.7天。出院时,1例患者残留压差为25毫米汞柱,其余患者无明显压差。平均随访时间为11个月(5 - 28个月)。出院1周后,1例患者出现手术伤口裂开。在最后一次随访时,所有患者均存活,吻合部位未观察到明显的残留压差或狭窄。无需再次干预。
一侧肺动脉起源异常是一种罕见但如果在生命早期进行手术则可能可治的病变。直接植入是一种具有良好短期效果的良好技术。