Arighi Andrea, Rango Mario, Bozzali Marco, Pietroboni Anna M, Fumagalli Giorgio, Ghezzi Laura, Fenoglio Chiara, Biondetti Pietro R, Bresolin Nereo, Galimberti Daniela, Scarpini Elio
Neurology Unit, Department of Pathophysiology and Transplantation, University of Milan, Foundation IRCCS Ca' Granda Ospedale Maggiore Policlinico, Via Francesco Sforza 35, 20121, Milan, Italy.
Neurology Unit, Department of Pathophysiology and Transplantation, University of Milan, Foundation IRCCS Ca' Granda Ospedale Maggiore Policlinico, Via Francesco Sforza 35, 20121, Milan, Italy; Magnetic Resonance Spectroscopy Center, Foundation IRCCS Ca' Granda Ospedale Maggiore Policlinico, Via Francesco Sforza 35, 20121, Milan, Italy.
PLoS One. 2015 Oct 19;10(10):e0140639. doi: 10.1371/journal.pone.0140639. eCollection 2015.
Posterior Cortical Atrophy (PCA) is a neurodegenerative disease characterized by a progressive decline in selective cognitive functions anatomically referred to occipital, parietal and temporal brain regions, whose diagnosis is rather challenging for clinicians. The aim of this study was to assess, using quantitative Magnetic Resonance Imaging techniques, the pattern of regional grey matter loss and metabolism in individuals with PCA to improve pathophysiological comprehension and diagnostic confidence.
We enrolled 5 patients with PCA and 5 matched controls who all underwent magnetic resonance imaging (MRI) and spectroscopy (MRS). Patients also underwent neuropsychological and cerebrospinal fluid (CSF) assessments. MRI data were used for unbiased assessment of regional grey matter loss in PCA patients compared to controls. MRS data were obtained from a set of brain regions, including the occipital lobe and the centrum semiovale bilaterally, and the posterior and anterior cingulate.
VBM analysis documented the presence of focal brain atrophy in the occipital lobes and in the posterior parietal and temporal lobes bilaterally but more pronounced on the right hemisphere. MRS revealed, in the occipital lobes and in the posterior cingulate cortex of PCA patients, reduced levels of N-Acetyl Aspartate (NAA, a marker of neurodegeneration) and increased levels of Myo-Inositol (Ins, a glial marker), with no hemispheric lateralization.
The bilateral but asymmetric pattern of regional grey matter loss is consistent with patients' clinical and neuropsychological features and with previous literature. The MRS findings reveal different stages of neurodegeneration (neuronal loss; gliosis), which coexist and likely precede the occurrence of brain tissue loss, and might represent early biomarkers. In conclusion, this study indicates the potential usefulness of a multi-parametric MRI approach for an early diagnosis and staging of patients with PCA.
后皮质萎缩(PCA)是一种神经退行性疾病,其特征是选择性认知功能逐渐下降,这些功能在解剖学上涉及枕叶、顶叶和颞叶脑区,对临床医生而言,其诊断颇具挑战性。本研究的目的是使用定量磁共振成像技术评估PCA患者区域灰质损失和代谢模式,以增进对病理生理学的理解并提高诊断信心。
我们招募了5例PCA患者和5名匹配的对照者,他们均接受了磁共振成像(MRI)和磁共振波谱(MRS)检查。患者还接受了神经心理学和脑脊液(CSF)评估。与对照组相比,MRI数据用于无偏评估PCA患者的区域灰质损失。MRS数据取自一组脑区,包括双侧枕叶和半卵圆中心,以及后扣带回和前扣带回。
基于体素的形态学分析(VBM)显示,双侧枕叶以及顶叶后部和颞叶存在局灶性脑萎缩,但在右半球更为明显。MRS显示,PCA患者的枕叶和后扣带回皮质中,N-乙酰天门冬氨酸(NAA,神经退行性变的标志物)水平降低,肌醇(Ins,一种胶质细胞标志物)水平升高,且无半球侧化现象。
区域灰质损失的双侧但不对称模式与患者的临床和神经心理学特征以及先前的文献一致。MRS结果揭示了神经退行性变的不同阶段(神经元丢失;胶质增生),这些阶段共存且可能先于脑组织损失的发生,可能代表早期生物标志物。总之,本研究表明多参数MRI方法对PCA患者的早期诊断和分期具有潜在的有用性。