Wrafter Paula F, Connelly Tara, Khan Jody Sultan Ali, Joyce William P
Department of Surgery, The Galway Clinic, Galway, Ireland.
University Hospital Galway, Galway, Ireland.
BMJ Case Rep. 2015 Oct 22;2015:bcr2015211706. doi: 10.1136/bcr-2015-211706.
Pseudomyxoma peritonei (PMP) is an uncommon clinical finding describing the intraperitoneal accumulation of abundant mucinous, jelly-like material. This entity may represent a spectrum of diseases ranging from mucinous ascites, commonly associated with ruptured epithelial tumours of the appendix, to frank mucinous carcinomatosis. In cases of appendiceal origin, the patient may present with signs and symptoms of acute appendicitis, and thus careful diagnosis must be made in order to correctly and appropriately guide management. This may include a combination of surgical debulking with or without intraperitoneal or systemic chemotherapy. We present a 52-year-old woman with a 4-month history of abdominal pain and distension with a previous appendicectomy 19 years earlier. Radiological and pathological investigations diagnosed a probable PMP secondary to ruptured appendicitis many years ago. We describe her unique case, with emphasis on length of time to diagnosis and clinical management by surgical cytoreduction alone.
腹膜假黏液瘤(PMP)是一种不常见的临床病症,描述的是腹腔内积聚大量黏液样、果冻状物质。该病症可能代表一系列疾病,从通常与阑尾上皮肿瘤破裂相关的黏液性腹水到明显的黏液性癌病。对于阑尾起源的病例,患者可能表现出急性阑尾炎的体征和症状,因此必须进行仔细诊断,以便正确且适当地指导治疗。这可能包括手术减瘤联合或不联合腹腔内或全身化疗。我们报告一名52岁女性,有4个月的腹痛和腹胀病史,19年前曾行阑尾切除术。影像学和病理检查诊断可能为多年前阑尾炎破裂继发的PMP。我们描述她的独特病例,重点关注诊断时间以及仅通过手术细胞减灭术的临床治疗情况。