Es Seddiki A, Rkain M, Messaoudi S, Benhadou H, Benajiba N
Service de pédiatrie, CHU Mohamed VI, Oujda, Maroc.
Service de pédiatrie, CHU Mohamed VI, Oujda, Maroc.
Arch Pediatr. 2015 Dec;22(12):1276-8. doi: 10.1016/j.arcped.2015.09.006. Epub 2015 Oct 29.
Plexiform neurofibroma is a rare benign tumor of the peripheral tissue cells developed in the perineurium. Often considered pathognomonic of neurofibromatosis type 1 (NF1 or von Recklinghausen disease), it can be solitary without NF1, especially in children. The diagnosis is essentially pathological and treatment is primarily surgical to avoid malignant degeneration. We report on a case of cervical solitary plexiform neurofibroma discovered in a 9-year-old child.
丛状神经纤维瘤是一种罕见的起源于神经束膜的外周组织细胞良性肿瘤。它常被认为是1型神经纤维瘤病（NF1或冯雷克林霍增氏病）的特征性表现，但也可以是孤立性的，不伴有NF1，尤其是在儿童中。诊断主要依靠病理检查，治疗主要是手术切除以避免恶变。我们报告了一例在一名9岁儿童中发现的颈部孤立性丛状神经纤维瘤病例。
