Sánchez Blanco J M, Miralles Sanchiz J, Galnares Barro R, Escribano Negueruela L
Rev Esp Enferm Apar Dig. 1989 Jan;75(1):73-7.
A case is presented of a 10-year-old female twin with a cystic liver mass that debuted as a painless epigastric mass. The lesion was excised by hepatectomy of segments II and III, confirming in the review of the cavity the presence of a common mesentery with cecocolonic malposition. The postoperative course was normal and clinical and echographic study of her twin sister disclosed no anomalies. The anatomopathologic study of the lesion revealed a tumor of difficult filiation that presented features of mesenchymal hamartoma together with others of biliary cystadenoma. The amount and nature of the stromal component, together with the patient's age at appearance, made us classify the case as mesenchymal hamartoma. The morphologic findings observed seem to support the histopathologetic theory of a congenital origin.
本文报告一例10岁女性双胞胎，其肝脏有一囊性肿物，最初表现为上腹部无痛性肿块。通过切除肝Ⅱ段和Ⅲ段进行肝切除术将病变切除，在对切除腔的检查中证实存在伴有盲结肠异位的共同肠系膜。术后过程正常，对其双胞胎姐妹的临床和超声检查未发现异常。病变的解剖病理学研究显示，这是一种难以明确谱系的肿瘤，具有间充质错构瘤的特征以及一些胆管囊腺瘤的特征。间质成分的数量和性质，以及患者出现症状时的年龄，使我们将该病例归类为间充质错构瘤。观察到的形态学结果似乎支持先天性起源的组织病理学理论。
