Arava Sudheer, Bagmar Saphalta, Jain Parul, Kumaran Muthu, Kumar Sanjeev, Ray Ruma
Department of Pathology, All India Institute of Medical Sciences, New Delhi, India.
Indian J Pathol Microbiol. 2015 Oct-Dec;58(4):531-3. doi: 10.4103/0377-4929.168867.
Myxomas are the most common benign cardiac tumors constituting approximately 75% of all the cardiac tumors. Rest 25% are malignant and sarcomas being the commonest. Among the sarcomas primary cardiac malignant peripheral nerve sheath tumors are extremely rare. They usually arise in relation to the branches of vagus or phrenic nerves, 5-42% being associated with neurofibromatosis type 1. Clinical signs and symptoms depend on the location and extent of involvement. Complete resection is the treatment of choice but local recurrence is common.
黏液瘤是最常见的心脏良性肿瘤，约占所有心脏肿瘤的75%。其余25%为恶性肿瘤，其中肉瘤最为常见。在肉瘤中，原发性心脏恶性外周神经鞘瘤极为罕见。它们通常与迷走神经或膈神经的分支有关，5% - 42%与1型神经纤维瘤病相关。临床症状和体征取决于病变的部位和范围。完整切除是首选的治疗方法，但局部复发很常见。
