Peña A
Department of Pediatric Surgery, Schneider Children's Hospital, Long Island Jewish Medical Center, New Hyde Park, NY 11042.
J Pediatr Surg. 1989 Jun;24(6):590-8. doi: 10.1016/s0022-3468(89)80514-7.
This report describes the author's personal experience in the surgical treatment of 54 patients. The approach is called posterior sagittal ano recto vagino urethroplasty (PSARVUP). Forty patients underwent a primary procedure, and 14 a secondary operation. The anatomic variations found were multiple, integrating a wide spectrum of defects. The posterior sagittal approach proved to be a good initial approach, and permitted complete repair of the defect in 47 patients. Seven patients required a laparotomy in addition. The length of the common channel varied from 0.5 to 7 cm. Common channels longer than 3 cm usually required some technical alternative to replace the vagina. In at least 34 cases, the vagina was reconstructed primarily without any additional technical manoeuvres. Different degrees of vaginal and uterine septation were found in 25 of 50 cases. Hydrocolpos was an associated defect in 14 of 49 patients. Sixty-eight percent of the patients had an important associated urological defect. Twenty-six patients were clinically evaluated without medical management, twenty-one of whom had voluntary bowel movements by the age of 3 years, but most of them had minor episodes of soiling. Nineteen patients had a normal sacrum, and five had urinary incontinence that was successfully managed by intermittent catheterization. Seven patients had a very abnormal sacrum, and five of them had urinary incontinence. Twenty patients underwent a late postoperative vaginoscopy, 14 of whom showed an adequate introitus and vagina, whereas five had different degrees of narrowing of the introitus. Six patients had a urethrovaginal fistula. One ureter was accidentally divided and one vagina had complete ischaemic necrosis.
本报告描述了作者对54例患者进行手术治疗的个人经验。该手术方法称为后矢状位肛门直肠阴道尿道成形术(PSARVUP)。40例患者接受了一期手术,14例接受了二期手术。发现的解剖变异多种多样,涵盖了广泛的缺陷。后矢状位入路被证明是一种良好的初始入路,47例患者的缺损得以完全修复。另外7例患者需要进行剖腹手术。共同通道的长度从0.5厘米到7厘米不等。长度超过3厘米的共同通道通常需要一些技术手段来重建阴道。至少34例患者在没有任何额外技术操作的情况下主要重建了阴道。50例患者中有25例发现了不同程度的阴道和子宫纵隔。49例患者中有14例伴有积水性阴道积血。68%的患者伴有重要的泌尿系统缺陷。26例患者未接受药物治疗进行了临床评估,其中21例在3岁时能够自主排便,但大多数患者有轻度污粪发作。19例患者骶骨正常,5例患者尿失禁通过间歇性导尿成功处理。7例患者骶骨非常异常,其中5例有尿失禁。20例患者术后晚期接受了阴道镜检查,其中14例阴道口和阴道正常,5例阴道口有不同程度的狭窄。6例患者有尿道阴道瘘。1例输尿管意外离断,1例阴道发生完全性缺血坏死。