Ferreiro Lucía, San-José Esther, Suárez-Antelo Juan, Abdulkader Ihab, Martínez-de-Alegría Anxo, González-Barcala Francisco-Javier, Valdés Luis
Department of Pulmonology, University of Santiago Hospital Complex, Santiago de Compostela, Spain.
Department of Clinical Analysis, University of Santiago Hospital Complex, Santiago de Compostela, Spain.
Clin Respir J. 2017 Nov;11(6):1079-1085. doi: 10.1111/crj.12421. Epub 2016 Jan 24.
Pleural epithelioid haemangioendothelioma (EHE) is a rare tumour that originates in the vascular endothelium with an intermediate degree of malignancy between haemangioma and angiosarcoma. Smoking and asbestos exposure are unproven risk factors and diagnosis is usually confirmed by thoracoscopy, since pleural fluid (PF) cytology is often not conclusive. Immunohistochemistry can also help to confirm the diagnosis. We report an 85-year-old patient with bilateral pleural EHE diagnosed by thoracoscopy, who debuted with a spontaneous bilateral haemothorax, the second described so far, and we conducted a thorough review of the literature to describe the clinical, radiological and prognostic features, as well as the PF, of this rare tumour.
胸膜上皮样血管内皮瘤（EHE）是一种罕见的肿瘤，起源于血管内皮，恶性程度介于血管瘤和血管肉瘤之间。吸烟和接触石棉作为危险因素尚未得到证实，诊断通常通过胸腔镜检查来确认，因为胸腔积液（PF）细胞学检查往往不能确诊。免疫组织化学也有助于确诊。我们报告了一名85岁双侧胸膜EHE患者，通过胸腔镜检查确诊，该患者首发症状为自发性双侧血胸，这是迄今为止报道的第二例，我们对文献进行了全面回顾，以描述这种罕见肿瘤的临床、放射学和预后特征以及胸腔积液情况。
