Talwar Sachin, Agarwal Palkesh, Choudhary Shiv Kumar, Airan Balram
Department of Cardiothoracic and Vascular Surgery, All India Institute of Medical Sciences, New Delhi, India
Department of Cardiothoracic and Vascular Surgery, All India Institute of Medical Sciences, New Delhi, India.
World J Pediatr Congenit Heart Surg. 2016 May;7(3):377-80. doi: 10.1177/2150135115590457. Epub 2015 Dec 23.
Patients with right atrial isomerism and total anomalous pulmonary venous connection (TAPVC) in a functionally univentricular heart are a challenging subset with a high mortality rate. We present the case of a patient with univentricular heart who had right atrial isomerism and associated mixed TAPVC (supracardiac, cardiac, and infracardiac). The anatomy was delineated precisely, and the patient underwent first-stage univentricular palliation consisting of TAPVC repair and bilateral bidirectional superior cavopulmonary anastomosis.
功能单心室合并右心房异构和完全性肺静脉异位连接（TAPVC）的患者是一个具有挑战性的亚组，死亡率很高。我们报告一例单心室患者，其合并右心房异构及相关的混合型TAPVC（心上型、心内型和心下型）。精确描绘了解剖结构，该患者接受了包括TAPVC修复和双侧双向腔肺吻合术的一期单心室姑息治疗。
