Kwon Hyoung Il, Paek Jun Oh, Kim Jeoung Eun, Ro Young Suck, Ko Joo Yeon
Hanyang University Hospital, Hanyang University College of Medicine, Seoul, Korea.
Hanyang University Hospital, Hanyang University College of Medicine, Seoul, Korea
Int J Low Extrem Wounds. 2016 Mar;15(1):92-5. doi: 10.1177/1534734615623432. Epub 2015 Dec 28.
Pyoderma gangrenosum (PG) is a rare, relapsing cutaneous disease with 4 distinctive clinical manifestations: ulcerative, bullous, pustular, and vegetative lesions. It mainly occurs in adults and is frequently associated with systemic diseases, most commonly inflammatory bowel disease, rheumatologic disease, or hematological dyscrasias. However, there have been no previous reports of PG in a patient with hereditary spherocytosis, a common inherited hemolytic anemia. We report here a unique case of PG in a 15-year-old boy with underlying hereditary spherocytosis.
坏疽性脓皮病（PG）是一种罕见的复发性皮肤病，有4种独特的临床表现：溃疡性、大疱性、脓疱性和增殖性皮损。它主要发生于成年人，常与全身性疾病相关，最常见的是炎症性肠病、风湿性疾病或血液系统发育异常。然而，此前尚无遗传性球形红细胞增多症（一种常见的遗传性溶血性贫血）患者发生PG的报道。我们在此报告一例15岁患有遗传性球形红细胞增多症的男孩发生PG的独特病例。
