Lim Ming Sheng, Lemmert Karla, Enjeti Anoop
Department of Haematology, Calvary Mater Newcastle, Waratah, New South Wales, Australia.
Department of Flow Cytometry, Pathology North Hunter, NSW Pathology, Newcastle, New South Wales, Australia.
BMJ Case Rep. 2016 Jan 20;2016:bcr2015214093. doi: 10.1136/bcr-2015-214093.
Blastic plasmacytoid dendritic cell neoplasm (BPDCN) is a rare and aggressive haematological malignancy in the elderly, with a high frequency of cutaneous and bone marrow involvement and poor prognosis. We report a case of BPDCN with classic presentation and discuss its treatment and the value of different investigation tools used in diagnosis and response assessment.
母细胞性浆细胞样树突状细胞肿瘤(BPDCN)是一种罕见的、侵袭性的老年血液系统恶性肿瘤,皮肤和骨髓受累频率高,预后差。我们报告一例具有典型表现的BPDCN病例,并讨论其治疗以及用于诊断和疗效评估的不同检查工具的价值。