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原发性胸膜肺滑膜肉瘤:一例报告

Primary pleuropulmonary synovial sarcoma: a case report.

作者信息

Yuan Lianfang, Guan Zhiyu, Dai Xuan, Xu Jie

机构信息

Department of Respiratory Medicine, Tianjin Hospital of ITCWM (Tianjin Nankai Hospital) Tianjin, China.

Department of Thoracic Surgery, The Second Hospital of Tianjin Medical University Tianjin, China.

出版信息

Int J Clin Exp Pathol. 2015 Nov 1;8(11):15426-8. eCollection 2015.

PMID:26823907
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC4713693/
Abstract

Pleuropulmonary synovial sarcoma (PPSS) is an extremely rare malignant tumor, which is increasingly recognized as a subtype of sarcoma with a distinctive chromosomal translocation specific to synovial sarcoma. It is often presents like any thoracic tumor with symptoms such as chest pain or cough. Here we report a case of PPSS in a 49-year-old woman presenting with cough, shortness of breath and chest pain. And who were found upon histologic examination of the resection specimen to have cystic primary pleuropulmonary synovial sarcoma.

摘要

胸膜肺滑膜肉瘤(PPSS)是一种极其罕见的恶性肿瘤,越来越被认为是肉瘤的一种亚型,具有滑膜肉瘤特有的独特染色体易位。它通常表现得与任何胸部肿瘤相似,有胸痛或咳嗽等症状。在此,我们报告一例49岁女性的胸膜肺滑膜肉瘤病例,该患者表现为咳嗽、气短和胸痛。经切除标本的组织学检查发现为囊性原发性胸膜肺滑膜肉瘤。

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本文引用的文献

1
CT imaging of primary pleuropulmonary synovial sarcoma.原发性胸膜肺滑膜肉瘤的 CT 影像学表现。
Clin Radiol. 2012 Sep;67(9):884-8. doi: 10.1016/j.crad.2012.02.009. Epub 2012 Apr 18.
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Synovial sarcoma: CT imaging of a rare primary malignant tumour of the thorax.滑膜肉瘤:胸部罕见原发性恶性肿瘤的 CT 影像学表现。
Radiol Med. 2011 Sep;116(6):868-75. doi: 10.1007/s11547-011-0692-7. Epub 2011 Jun 4.
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Primary pleuropulmonary synovial sarcoma.原发性胸膜肺滑膜肉瘤
Clin Lung Cancer. 2008 Sep;9(5):257-61. doi: 10.3816/CLC.2008.n.040.
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From the archives of the AFIP: Imaging of synovial sarcoma with radiologic-pathologic correlation.源自武装部队病理研究所档案:滑膜肉瘤的影像学表现及其与病理的相关性
Radiographics. 2006 Sep-Oct;26(5):1543-65. doi: 10.1148/rg.265065084.
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From the archives of the AFIP: Pleuropulmonary synovial sarcoma.源自武装部队病理研究所档案:胸膜肺滑膜肉瘤。
Radiographics. 2006 May-Jun;26(3):923-40. doi: 10.1148/rg.263055211.
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Chest wall tumors: radiologic findings and pathologic correlation: part 2. Malignant tumors.胸壁肿瘤:影像学表现与病理对照:第2部分。恶性肿瘤。
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Primary pleuropulmonary synovial sarcoma: reappraisal of a recently described anatomic subset.原发性胸膜肺滑膜肉瘤:对最近描述的一种解剖学亚型的重新评估
Cancer. 2002 Jan 15;94(2):459-69. doi: 10.1002/cncr.10188.
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Synovial sarcoma: a clinicopathologic, staging, and prognostic assessment.滑膜肉瘤:临床病理、分期及预后评估
J Clin Oncol. 2000 Nov 15;18(22):3794-803. doi: 10.1200/JCO.2000.18.22.3794.