Ashby Elizabeth, Montpetit Kathleen, Hamdy Reggie C, Fassier François
Shriners Hospital for Children.
Department of Paediatric Surgery, Division of Paediatric Orthopaedics, McGill University, Montreal, QC, Canada.
J Pediatr Orthop. 2018 Jan;38(1):54-59. doi: 10.1097/BPO.0000000000000724.
The impact of corrective forearm surgery on functional ability in children with osteogenesis imperfecta (OI) has not previously been reported. This study addresses this issue.
A retrospective chart review was conducted on 19 children with OI who underwent 22 corrective forearm procedures between 1996 and 2013. Functional ability was assessed preoperatively and every year postoperatively using the Pediatric Evaluation of Disability Inventory (PEDI).
The mean PEDI self-care score increased by 6.8 (P=0.017) and the mean PEDI mobility score increased by 7.2 (P=0.020) at 1-year postsurgery. Functional gains were greater in moderate OI (types IV, V, and VI) than in severe OI (type III). Improved function was maintained in the majority of cases at a mean of 8.9 years postcorrection.
Corrective forearm surgery in children with OI leads to improved functional ability.
Level IV.
既往尚无关于矫正性前臂手术对成骨不全(OI)患儿功能能力影响的报道。本研究旨在解决这一问题。
对19例在1996年至2013年间接受了22例矫正性前臂手术的OI患儿进行回顾性病历审查。术前及术后每年使用儿童残疾评估量表(PEDI)评估功能能力。
术后1年,PEDI自我护理评分平均提高6.8(P = 0.017),PEDI活动评分平均提高7.2(P = 0.020)。中度OI(IV、V和VI型)的功能改善比重度OI(III型)更大。在大多数病例中,矫正后平均8.9年功能改善得以维持。
OI患儿的矫正性前臂手术可提高功能能力。
IV级。