一名86岁患者的门体分流性脑病：一项临床挑战。
Portosystemic encephalopathy in an 86-year-old patient : a clinical challenge.
作者信息
Merola E, Cao M, La Starza S, Delle Fave M M, Tavanti F, Sergi D, Marignani M
出版信息
Acta Gastroenterol Belg. 2016 Mar;79(1):58-9.
PMID:26852766
Abstract
Abernethy malformations are rare vascular abnormalities, classified into two types : type 1 if the portal vein is absent, type 2 when the portal blood is diverted into vena cava through a hypoplastic portal vein. These conditions present symptoms related to portosystemic shunting, and usually become clinically evident in children or young adults. Here we report the first case of Abernethy malformation diagnosed in an 86-year-old female patient affected by portosystemicencephalopaty.
摘要
阿伯内西畸形是罕见的血管异常，分为两种类型：1型是门静脉缺失，2型是门静脉血液通过发育不全的门静脉分流至腔静脉。这些病症会出现与门体分流相关的症状，通常在儿童或年轻人中变得临床明显。在此，我们报告首例在一名患有门体性脑病的86岁女性患者中诊断出的阿伯内西畸形病例。
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