Maccari Uberto, Rosini Costanza F, Scala Raffaele, Magnolfi Anna Lisa, Felici Massimo, Bolognese Leonardo
U.O.C. e U.T.I.P. Pneumologia.
Dipartimento Cardiovascolare e Neurologico.
G Ital Cardiol (Rome). 2016 Jan;17(1):58-61. doi: 10.1714/2140.23194.
Vascular rings are rare anomalies accounting for 1% to 3% of all congenital heart diseases with a similar frequency in both sexes, which can result in a variable degree of extrinsic compression of the trachea and esophagus. We report the case of a 46-year-old woman with symptomatic dyspnea and double aortic arch that caused esophageal tracheal compression. Considering the little impact of the functional vascular anomaly in our case, a conservative approach was adopted with clinical and functional annual follow-up.
血管环是罕见的先天性心脏畸形，占所有先天性心脏病的1%至3%，男女发病率相似，可导致气管和食管不同程度的外部受压。我们报告了一例46岁有症状性呼吸困难且双主动脉弓导致食管气管受压的女性病例。鉴于我们病例中功能性血管异常影响较小，我们采取了保守治疗方法，并进行每年一次的临床和功能随访。
