Arava Sudheer, Breta Monika, Madan Karan, Nath Devajit, Mehta Swapnil, Jain Deeapli
Department of Pathology, All India Institute of Medical Sciences, New Delhi, India.
Indian J Pathol Microbiol. 2016 Jan-Mar;59(1):69-71. doi: 10.4103/0377-4929.178226.
Liposarcomas are extremely rare in the mediastinum. Patients usually present late due to the compressive effect of the tumor on the adjacent structures. Severity of the symptoms depend mainly on the size of the tumor and the structure it infiltrates. Well differentiated slow growing liposarcomas are the most common ones in the mediastinum followed by dedifferentiated and poorly differentiated ones. These tumors have bad prognosis because of incomplete surgical excision due to its inaccessible location. Hence these patients should be kept under close follow up because of high recurrent rates. Here we are presenting a rare case of anterior mediastinal sclerosing liposarcoma in a 77 year old male.
脂肪肉瘤在纵隔中极为罕见。由于肿瘤对相邻结构的压迫作用,患者通常就诊较晚。症状的严重程度主要取决于肿瘤的大小及其浸润的结构。高分化、生长缓慢的脂肪肉瘤是纵隔中最常见的类型,其次是去分化和低分化脂肪肉瘤。由于其位置难以触及,手术切除不完全,这些肿瘤预后较差。因此,由于复发率高,这些患者应密切随访。在此,我们报告一例77岁男性前纵隔硬化性脂肪肉瘤的罕见病例。