Iwata Yusuke, Kojima Ai, Nakayama Yuki, Omoya Kentaro, Kuwahara Takashi, Takeuchi Takamasa
1 Department of Pediatric Cardiac Surgery, Children's Medical Center, Gifu Prefectural General Medical Center, Gifu, Japan.
2 Department of Pediatric Cardiology, Children's Medical Center, Gifu Prefectural General Medical Center, Gifu, Japan.
Asian Cardiovasc Thorac Ann. 2017 May;25(4):292-295. doi: 10.1177/0218492316641535. Epub 2016 Mar 27.
Biatrial drainage of the right superior vena cava resulting from a sinus venosus defect is a rare congenital malformation. It can result in severe desaturation although a sinus venosus defect usually presents as a left-to-right shunt. A male baby was noted to have cyanosis while nursing and was referred to us for medical treatment on his second day of life. Echocardiography showed that most of the blood flowing through the superior vena cava drained into the left atrium. He underwent successful surgery to correct this defect at the age of 2 years.
静脉窦缺损导致右上腔静脉双心房引流是一种罕见的先天性畸形。尽管静脉窦缺损通常表现为左向右分流，但它可导致严重的血氧饱和度降低。一名男婴在哺乳时被发现有发绀症状，并在出生第二天被转诊至我院接受治疗。超声心动图显示，流经上腔静脉的大部分血液流入左心房。他在2岁时接受了成功的手术来纠正这一缺陷。
