一名35岁女性的原发性肺动脉瓣平滑肌肉瘤
Primary Pulmonary Valve Leiomyosarcoma in a 35-Year-Old Woman.
作者信息
Vakilian Farveh, Shabestari Mahmoud M, Poorzand Hoorak, Teshnizi Mohammad Abbasi, Allahyari Abolghasem, Memar Bahram
出版信息
Tex Heart Inst J. 2016 Feb 1;43(1):84-7. doi: 10.14503/THIJ-14-4748. eCollection 2016 Feb.
Abstract
Primary cardiac leiomyosarcomas are rare, with a high incidence of local recurrence. Herein, we report the case of a 35-year-old woman who was admitted with right ventricular failure and suspected pulmonary embolism. Upon echocardiography, we detected a mass in the pulmonary trunk that involved the pulmonary valve and led to valvular stenosis. The optimal protocol for treating these tumors is as yet unclear. Complete resection can rarely be achieved. However, palliative surgery is usually undertaken because many patients present with mechanical obstruction, such as significant pulmonary stenosis.
摘要
原发性心脏平滑肌肉瘤罕见，局部复发率高。在此，我们报告一例35岁女性患者，因右心衰竭和疑似肺栓塞入院。经超声心动图检查，我们在肺动脉主干发现一个肿块，累及肺动脉瓣并导致瓣膜狭窄。目前尚不清楚治疗这些肿瘤的最佳方案。很少能实现完全切除。然而，通常会进行姑息性手术，因为许多患者存在机械性梗阻，如严重的肺动脉狭窄。
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