Powell R W
Clinical Investigation Center, Naval Hospital, San Diego, California.
Am Surg. 1989 Apr;55(4):212-8.
Three male adolescents, ages 13, 15, and 17 years, presented with complications of their Hirschsprung's disease, including acute enterocolitis with sepsis, chronic enterocolitis with anemia and leukocytosis, and severe fecal impaction. All had experienced delay in diagnosis resulting from either physician error in diagnosis or physician misinformation concerning the surgical treatment of the disease. These three patients illustrate some of the pitfalls in the diagnosis and surgical management of patients with Hirschsprung's disease. Misinformation concerning the surgical correction of this disease still exists, and these patients emphasize the necessity of continued, updated information in the diagnosis, management, and outcome of patients with Hirschsprung's disease.
三名男性青少年,年龄分别为13岁、15岁和17岁,患有先天性巨结肠并发症,包括急性小肠结肠炎伴败血症、慢性小肠结肠炎伴贫血和白细胞增多症,以及严重的粪便嵌塞。所有患者均因医生诊断错误或关于该疾病手术治疗的错误信息而导致诊断延误。这三名患者说明了先天性巨结肠患者诊断和手术管理中的一些陷阱。关于该疾病手术矫正的错误信息仍然存在,这些患者强调了在先天性巨结肠患者的诊断、管理和预后方面持续更新信息的必要性。