鼻腔封闭术治疗遗传性出血性毛细血管扩张症继发鼻出血
Nasal closure for the treatment of epistaxis secondary to hereditary hemorrhagic telangiectasia.
作者信息
Sena Esteves Sara, Cardoso Carla, Silva Ana, Abrunhosa José, Almeida E Sousa Cecília
机构信息
Department of Otolaryngology, Oporto Hospital Center, Oporto, Portugal.
Department of Otolaryngology, Oporto Hospital Center, Oporto, Portugal.
出版信息
Acta Otorrinolaringol Esp. 2016 Nov-Dec;67(6):345-348. doi: 10.1016/j.otorri.2015.12.002. Epub 2016 Apr 11.
UNLABELLED
Hereditary hemorrhagic telangiectasia (HHT), also known by the eponym Osler-Weber-Rendu syndrome, is an autosomal dominant disorder characterised by the presence of multiple arteriovenous malformations (AVMs) affecting multiple organs. Many procedures have been used for epistaxis control in patients with this disorder. The objective of this study was to report the treatment of severe HHT-related epistaxiswith the modified Young's procedure.
MATERIALS AND METHODS
We describe the treatment of 4 patients with severe blood-transfusion-dependent epistaxis who underwent a modified Young's procedure in a tertiary hospital. The nasal closure was bilateral and complete in all cases. All patients were followed for 12 months or longer.
RESULTS
The procedure was well tolerated and complete cessation of bleeding was achieved in all the patients.
CONCLUSION
Young's technique is a safe surgical procedure, well tolerated by patients with severe epistaxis and HHT.
未标注
遗传性出血性毛细血管扩张症（HHT），也被称为奥斯勒-韦伯-伦杜综合征，是一种常染色体显性疾病，其特征是存在影响多个器官的多发动静脉畸形（AVM）。已经有多种方法用于控制该疾病患者的鼻出血。本研究的目的是报告采用改良杨氏手术治疗严重的HHT相关性鼻出血。
材料与方法
我们描述了4例严重依赖输血的鼻出血患者在一家三级医院接受改良杨氏手术的治疗情况。所有病例均为双侧且完全封闭鼻腔。所有患者均随访12个月或更长时间。
结果
该手术耐受性良好，所有患者均实现了出血完全停止。
结论
杨氏技术是一种安全的外科手术，严重鼻出血和HHT患者对其耐受性良好。
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