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埃布斯坦畸形修复术后心肌内血肿

Intramyocardial Hematoma After Ebstein Anomaly Repair.

作者信息

Lim Joel Kian Boon, Lee Jan Hau, Mok Yee Hui, Chen Ching Kit, Loh Yee Jim

机构信息

1 Department of Pediatrics, KK Women's and Children's Hospital, Singapore.

2 Children's Intensive Care Unit, Department of Pediatric Subspecialties, KK Women's and Children's Hospital, Singapore.

出版信息

World J Pediatr Congenit Heart Surg. 2017 Jan;8(1):117-120. doi: 10.1177/2150135115623528. Epub 2016 Jun 22.

DOI:10.1177/2150135115623528
PMID:27098604
Abstract

Intramyocardial hematoma is a rare condition and is an incomplete form of myocardial rupture, which may occur after myocardial infarction, cardiac surgery, trauma, percutaneous coronary intervention, or spontaneously. We describe a case of a 16-year-old girl with intramyocardial hematoma mimicking an intracavitary thrombus following repair of Ebstein anomaly. The intramyocardial hematoma was incorrectly diagnosed on echocardiography as a right ventricular thrombus, and the true nature of the lesion was only realized during repeat surgical intervention for severe tricuspid regurgitation. The hematoma was managed conservatively and spontaneously resolved.

摘要

心肌内血肿是一种罕见的病症,是心肌破裂的不完全形式,可能发生在心肌梗死、心脏手术后、创伤、经皮冠状动脉介入治疗后或自发出现。我们描述了一例16岁女孩的病例,该女孩在埃布斯坦畸形修复术后出现心肌内血肿,酷似心腔内血栓。心肌内血肿在超声心动图检查中被误诊为右心室血栓,直到因严重三尖瓣反流进行再次手术干预时才发现病变的真实性质。该血肿采取保守治疗并自行消退。

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